A amelogénese imperfeita constitui uma anomalia de desenvolvimento do esmalte, de carácter hereditário. A sua prevalência é de , podendo o esmalte. Amelogenesis imperfecta (AI) is a congenital disorder that presents with a rare abnormal formation of the enamel or external layer of the crown of teeth. 19 jul. O objetivo deste artigo foi apresentar uma revisão de literatura sobre tratamento restaurador conservador na amelogênese imperfeita.

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This is an open-access article distributed under the terms of the Creative Commons Impegfeita License. It is predominantly a sensorimotor dysfunction, involving disorders in muscle tonus, posture, and voluntary movement 4.

Amelogenesis imperfecta

It is imperative that she takes part in a program of periodic and preventive maintenance. Autosomal recessive inheritance means two copies of the gene in each cell are altered. However, the authors of this systematic review failed to identify the best intervention. Explicit use of et al. According to her adoptive parents, until the age of two the child was only given liquid diet through a syringe, presenting severe malnutrition.

Stomatos – Amelogenese imperfecta em uma criança com paralisia cerebral

Phys Ther ; In these appointments, the conditions of the GIC restorations of the posterior teeth will amelogejese evaluated. Case Report The patient authorized publication of this case and written informed consent was obtained from this his parents. The dental care of patients affected by disabilities is often out of the usual routine, requiring ameogenese knowledge, greater sensitivity, increased attention and adequate environment 7.

The dental caregiver must be aware of speech disorders and also lack of correspondence between the chronological age of the patient and his actions. Enamel appears less radioopaque compared to dentine on radiographs. For the clinical procedures, mouth-openers made with wooden tongue depressors ameloegnese gauze or a PVC pipe were used, in addition to continuous use of an aspirator tube Figure 5A and 5B.

For these restorations, prefabricated acetate crowns were selected. An intraoral examination revealed teeth with alterations in size and shape, yellow-brown discoloration Fig.


Views Read Edit View history. The case shows that it is possible to perform complex dental care of disabled patients in an outpatient environment. It was concluded that the adhesive system for tooth desensitization had an immediate effect and maintained its effectiveness during ameloegnese month follow-up period.

No intraoral anomalies are exclusive to people with cerebral palsy, but they can be more severe than in the general population. Amelogenesis imperfecta AI is a hereditary anomaly of the enamel, which affects both dentitions and may cause tooth sensitivity, loss of vertical dimension, enamel deficiencies, pulp calcification, failed tooth eruption, impaction of permanent impfrfeita and aesthetic commitment 12. J Am Dent Assoc ; The enamel may have formation disorders or even defects in its mineral and protein content 1,2.

The current medical history of the patient do not present further systemic alterations, and she is not under any medication. The GIC is an important material in the minimally invasive dental practice, and it stands out by its adhesion to the amflogenese structure, linear thermal expansion coefficient similar to the tooth, biocompatibility, fluoride release, and easy technique Paediatr Dent ; Alterations can also be observed on the sucked finger Figure 2.

Cerebral palsy, which is the condition affecting the previously mentioned patient, is a non-hereditary lesion that affects the nervous system before the age of two, during pre- peri- or postnatal period. The literature presents different treatments that use all types of glass ionomer cements, stainless steel crowns, amalgam restorations, adhesive restorations, metal-ceramic crowns, prefabricated resin veneer, and multiple extractions requiring an overdenture 7, Genes and related proteins involved in amelogenesis imperfecta.

At the buccal, lingual or palatal and occlusal faces Figs. Recent genetic studies amelogenesw that the cause of a significant proportion of amelogenesis imperfecta cases remains to be discovered.

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Study models were made to complement the clinical examination. A fonoaudiologia na Paralisia Cerebral: Nephrocalcinosis is often asymptomatic but can progress during late childhood or early adulthood to impaired renal function e. Restoring function and esthetics in a patient with amelogenesis imperfecta: During anamnesis, his mother did not know if anyone else in the family had the same problem and reported that amelogemese son was diagnosed with attention-deficit hyperactivity disorder. In this clinical case, the patient presents intellectual disability, no speech and comprehension, and increased muscle tonus, in addition to compromised lower limbs, causing the patient to use a wheelchair.


AI can be classified according to phenotype and clinical aspect as follows: Composite resin short-post technique for primary anterior teeth.

Infobox medical condition new All articles with unsourced statements Articles with unsourced statements from June Association between characteristics of locomotion and accomplishment of life habits in children with cerebral palsy. Some AI patients can be bullied due to the aesthetic compromise caused by this condition. Iimperfeita documents contained in this web site impeffeita presented for information purposes only.

Rev Bra Crescimento e Desenvolvimento Hum ; Preventive and restorative dental care is very important as well as considerations for esthetic issues since the crown are yellow from exposure of dentin due to enamel loss.

How to cite this article. Health care resources for this disease Expert centres Diagnostic tests 3 Patient organisations 22 Orphan drug s 0.

Interventions for the restorative care of amelogenesis imperfecta in children and adolescents. Moreover, the difficult access to dental services and the fact that those services are often precarious, added to the lack of qualified personnel dental surgeons and dental assistants can be mentioned as problems related imperfeia this matter.

Clinical examination revealed the presence of generalized bacterial plaque on the surface of the teeth. Revista Odontologica Bras Central ; International classification of function and disability, Beta-2 Version.

CP patients can present disorders in speech development because of the alterations on expressive-motor aspects of language; nevertheless, comprehension is preserved in some cases 8.